Quadricuspid Aortic Valve: Incidental detection on Intraoperative Trans- oesophageal Echocardiography(TEE) | ||||
| The Egyptian Journal of Cardiothoracic Anesthesia | ||||
| Articles in Press, Accepted Manuscript, Available Online from 19 May 2025 | ||||
| Document Type: Case reports | ||||
| DOI: 10.21608/ejca.2024.276931.1003 | ||||
 View on SCiNiTO | ||||
| Authors | ||||
Vishnu Datt   1; Diksha Datt2; Saket Agarwal3; Isha Singh4; Suman Rani5; Aditya Rathee6
| ||||
| 1SGT Medical College and Hospital, Gurugram | ||||
| 2MD student PSM, SGT Medical College, Gurugram, Haryana | ||||
| 3GIPMER, New Delhi | ||||
| 4MD student Anaesthesiology, SGT Hospital, gurugram | ||||
| 5MD student Anaesthesiology, SGT Medical college, Gurugram | ||||
| 6SR, Anaesthesiology, SGT Medical College, Gurugram, Haryana | ||||
| Abstract | ||||
| The quadricuspid aortic valve (QAV) is one of the rare congenital cardiac anomalies with an incidence of 0.00028-0.00033% in autopsy series, 0.0059-0.0065% for patients undergoing trans-thoracic echocardiography (TTE) assessment and 0.05-1% for those undergoing aortic valve replacements for aortic regurgitation (AR) [1]. QAV is frequently an isolated congenital anomaly, but may also be associated with other cardiac anomalies like; coronary anomalies, coronary artery abnormalities, ventricular septal defect, patent ductus arteriosus, pulmonary stenosis(PS), ruptured sinus of valsalva, complete heart block, hypertrophic cardiomyopathy and Ehlers–Danlos syndrome.[2] Anatomically there are three equal cusps and one small cusp. However, There is no correlation between the anatomy and functional status of the aortic cusps. The functional status of QAV is predominantly regurgitant, whereas pure stenotic QAV can be as few as in only 0.7% of the patients. Perioperative TEE examination in a 2 year- old, female child undergoing cardiac correction surgery incidentally detected the normally functioning QAV characterized by four cusps of equal size, associated with OS -ASD, supravalvular pulmonary stenosis(PS) , severe tricuspid regurgitation (TR) and right ventricular(RV) dysfunction | ||||
| Keywords | ||||
| Quadricuspid aortic valve; rare anomaly; TEE; supravalvular PS; OS- ASD | ||||
|
Statistics Article View: 39 |
||||
