Hypertrophic cardiomyopathy in a Behçet’s Patient; a Chance or Chess | ||||
| The Egyptian Journal of Hypertension and Cardiovascular Risk | ||||
| Article 7, Volume 15, Issue 1, March 2024 PDF (600.45 K) | ||||
| Document Type: Clinical Case | ||||
| DOI: 10.21608/tejhcr.2025.369437.1008 | ||||
 View on SCiNiTO | ||||
| Authors | ||||
Beshoy Ayoub Asaeid Yacoub   1; Mina Saba 2
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| 1Department of cardiovascular medicine, kasralainy hospital, Cairo University | ||||
| 2Southeast Health, AL, USA | ||||
| Abstract | ||||
| Hypertrophic Cardiomyopathy (HCM) is an inherited autosomal dominant cardiomyopathy characterized by marked genotypic and phenotypic heterogeneity. On the other hand, Behçet's disease is a recurrent multisystemic inflammatory disorder associated with vasculitis and recurrent arterial and venous thrombosis. The etiology of BD is linked to viral, toxic, bacterial, and immunological factors. To date, no cases have been reported describing an association between Behçet’s disease and Hypertrophic Cardiomyopathy (HCM). We present a case of a 31-year-old male with Behçet’s disease and a history of recurrent DVT who presented with atypical chest pain and dyspnea that has been ongoing for 1 year. An echocardiography study revealed an asymmetrical increase in left ventricular wall thickness and significant provocable left ventricular outflow tract obstruction (LVOTO). A diagnosis of hypertrophic obstructive cardiomyopathy was confirmed by cardiac magnetic resonance (CMR). The potential relationship between Behçet’s disease and hypertrophic cardiomyopathy remains unclear. While this coexistence may be purely coincidental, the absence of previous reports on this association raises the possibility of an underlying pathophysiological link that has yet to be explored. | ||||
| Keywords | ||||
| Behçet’s disease; HCM; LVOTO | ||||
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