Mauriac Syndrome; A Rare Complication of T1 DM | ||
Egyptian Society of Diabetes and Lipidology Journal | ||
Volume 4, Issue 2, October 2024 PDF (1.4 M) | ||
Document Type: Case Report | ||
DOI: 10.21608/esdlj.2024.456255 | ||
Abstract | ||
Mauriac syndrome (MS) is characterized by excessive intrahepatic glycogen deposition, attributed to severe hyperglycemia which diffuses by insulin-independent GLUT 2 to be trapped inside hepatocytes as G -6 phosphate. It can rarely occur in poorly controlled T1 diabetic adolescents and is complicated by hepatomegaly, short stature, delayed puberty and hypertriglyceridemia | ||
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