Glanzmann’s Thrombasthenia: Epistaxis Treatment and Outcomes in Children | ||||
| The Egyptian Journal of Hospital Medicine | ||||
| Article 14, Volume 70, Issue 6, January 2018, Page 961-964 PDF (437.25 K) | ||||
| Document Type: Original Article | ||||
| DOI: 10.21608/ejhm.2018.10884 | ||||
 View on SCiNiTO | ||||
| Authors | ||||
Thikra Mohammed Alblowi  ; Fahad Nashmi Alshammari; Bashayer Aqeel Alshammari; Ahmed Ali Elazab; Thamer Menwer Albilasi; Hind Jaza Alotaibi
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| Hail University, Collage of Medicine | ||||
| Abstract | ||||
| Background: Glanzmann’s Thrombasthenia (GT) is a rare inherited blood clotting (coagulation) disorder characterized by the impaired function of specialized cells (platelets) which are essential for proper blood clotting. Objectives: The present study aimed to assess the management steps of epistaxis in children with GM disease and assess the clinical outcome and the success rate or field of management. Methods: Data was taken via scanning all the patients’ files in ENT clinic and 4 children with GM were identified as receiving therapy. Furthermore, data collected from each file were primary complaint needing a duration of hospitalization, intensive care unit (ICU) admission, coagulation management, hematologic results, medical therapy administration, blood products transfusion and the surgical intervention performed. Results: With a total of 25 hospital presentations, the highest percentage of the present symptoms was for epistaxis with 68% (17), then 16% (4) for gingival bleeding and 8% for each of menorrhagia and hematemesis. Conclusion and recommendation: Our study carried out the most effective technique that control epistaxis is Fresh Frozen (FFP) Plasma. The epistaxis in GT should be concern as sever threating life condition and should be managed with effective treatment. | ||||
| Keywords | ||||
| Glanzmann’s Thrombasthenia; epistaxis; disorder | ||||
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