The Fast and Furious, a Rare Case of Primary Burkitt’s Lymphoma of the Skull Base
Goh, B., Bee-See, G., Dayana, Z., Yean, K., Azizi, A. (2018). The Fast and Furious, a Rare Case of Primary Burkitt’s Lymphoma of the Skull Base. EKB Journal Management System, 19(2), 64-67. doi: 10.21608/ejentas.2018.3086.1005
Bee-See Goh; Goh Bee-See; Zahedi Farah Dayana; Kew Thean Yean; Abu Bakar Azizi. "The Fast and Furious, a Rare Case of Primary Burkitt’s Lymphoma of the Skull Base". EKB Journal Management System, 19, 2, 2018, 64-67. doi: 10.21608/ejentas.2018.3086.1005
Goh, B., Bee-See, G., Dayana, Z., Yean, K., Azizi, A. (2018). 'The Fast and Furious, a Rare Case of Primary Burkitt’s Lymphoma of the Skull Base', EKB Journal Management System, 19(2), pp. 64-67. doi: 10.21608/ejentas.2018.3086.1005
Goh, B., Bee-See, G., Dayana, Z., Yean, K., Azizi, A. The Fast and Furious, a Rare Case of Primary Burkitt’s Lymphoma of the Skull Base. EKB Journal Management System, 2018; 19(2): 64-67. doi: 10.21608/ejentas.2018.3086.1005

The Fast and Furious, a Rare Case of Primary Burkitt’s Lymphoma of the Skull Base

Egyptian Journal of Ear, Nose, Throat and Allied Sciences
Article 6, Volume 19, Issue 2, June 2018, Page 64-67  XML PDF (845.03 K)
Document Type: Case report
DOI: 10.21608/ejentas.2018.3086.1005
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Authors
Bee-See Goh email 1; Goh Bee-See2; Zahedi Farah Dayana2; Kew Thean Yean3; Abu Bakar Azizi4
1National University Of Malaysia
2Otolaryngology, National University Of Malaysia
3Radiology, National University Of Malaysia
4Neurosurgery, National University Of Malaysia
Abstract
Burkitt’s Lymphoma of the head and neck region commonly involves the facial bones in its endemic variant and Waldeyer’s ring in the sporadic variant. Base of skull is a rare site for primary Burkitt’s lymphoma, with nasal and neuro-ophthalmology symptoms as its presentation. We report a case of a three year-old girl presented with sudden and progressive bilateral eye blindness associated with bilateral inward squint, proptosis and nasal blockage. Imaging study demonstrated a large anterior skull base lesion with extension into ethmoid and sphenoid sinuses. Tumor was removed via open surgery and histopathological examination confirmed the diagnosis of Burrkitt’s lymphoma. Patient had permanent bilateral blindness postoperatively and succumbed two months after the initial presentation due to the agressiveness of the tumor. The late presentation, aggressiveness of the disease and lack of financial support contribute to her untimely demise. Burkitt’s Lymphoma of the base of skull warrants early tissue diagnosis by means of surgical intervention to ensure prompt commencement of treatment.
Keywords
Blindness; Burkitt’s Lymphoma; nasal blockage; Skull base
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