Feminizing genitoplasty in childhood: aiming for achievable outcomes | ||||
| Annals of Pediatric Surgery | ||||
| Volume 16, Issue 1, January 2020 PDF (2.42 MB) | ||||
| DOI: 10.1186/s43159-020-00044-w | ||||
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| Author | ||||
| Stella Nimanya | ||||
| Abstract | ||||
| Background Early genital reconstruction may be recommended in cases of congenital adrenal hyperplasia to avoid the stigma that can affect these individuals with variable degrees through different cultures. However, the separation and mobilization of a high vagina has remained challenging with less satisfactory surgical outcomes. Therefore, the value of early vaginal reconstruction has been questioned in favour of delaying the whole repair after puberty. In this report, the author has adopted the third option in-between, which comprises early reconstruction of the external genitalia and delaying the more challenging vaginal reconstruction (if needed) to be performed after puberty. Results The study included ten consecutive cases of CAH who underwent feminizing genitoplasty during the period 2016 through 2019. Their age at operation ranged from 8 to 84 months (mean 31; median 15). Conclusion In cases of congenital adrenal hyperplasia, reduction clitoroplasty combined with partial urogenital sinus mobilization can achieve predictable and satisfactory outcomes. In about 50% of cases, this approach is sufficient to bring the vagina down to the perineum. In the other half of cases with higher vagina, the possibility of satisfactory sinus intercourse can be studied when these girls grow and become sexually active; otherwise, a delayed vaginal reconstruction may turn to be necessary. | ||||
| Keywords | ||||
| Congenital adrenal hyperplasia; clitoris; Vestibuloplasty; urogenital sinus; genitalia | ||||
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