CLINICAL FINDINGS OF BASAL CELL NEVUS SYNDROME. | ||||
Egyptian Dental Journal | ||||
Volume 70, Issue 2, April 2024, Page 1127-1137 PDF (3.54 MB) | ||||
Document Type: Original Article | ||||
DOI: 10.21608/edj.2024.258875.2854 | ||||
View on SCiNiTO | ||||
Authors | ||||
ALTAIB ABD ALRAZIK MOHAMMED 1; Eisa M Hegazy 2; AMR ABD ALMOEZ MAHMOUD 3; AHMED BASTAWY MOHAMMED 4 | ||||
1Assistant Professor of Oral and Maxillofacial Surgery, Faculty of Oral and Dental Medicine, South Valley University | ||||
2Assistant Professor, Department of Dermatology,Venereology and Andrology, Faculty of Medicine South Valley University | ||||
3Assistant Lecturer of Oral and Maxillofacial Pathology | ||||
4Lecturer Of Pediatric Dentistry and Public Health Faculty of Oral and Dental Medicine, South Valley University | ||||
Abstract | ||||
Abstract Background Basal cell nevus syndrome or Gorlin syndrome is a rare genetic autosomal dominant disorder associated with different neoplasms that may be aggressive with further aging so that earlier diagnosis of this syndrome is crucial Aim of the study The aim of this study is to present different clinical pictures and diagnostic means to facilitate identification of patients affected by basal cell nevus bifid rib syndrome Subject and methods Seven patients presented with basal cell nevus syndrome were investigated through reporting medical and dental history, clinical and radiological examinations, histopathological investigations , routine laboratory investigations and referral to different specialties as dermatology , neurosurgery and orthopedics . Results All the patients presented with odontogenic keratocysts , bifid ribs, skin nevi, and skeletal disorders .. with three patients having family history affected by the same findings . Conclusion basal cell nevus bifid rib syndrome has different clinical presentations and many specialists of different specialties as maxillofacial surgery, neurosurgery , dermatology and others must be aware of them ,also affected patients need frequent, follow up to avoid any complications associated with this syndrome .. | ||||
Keywords | ||||
Basal cell; nevus; bifid rib; keratocyst; syndrome | ||||
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