Pain Assessment among Egyptian Children with Transfusion-Dependent Hemoglobinopathies: Pilot Study | ||||
Mansoura Nursing Journal | ||||
Volume 11, Issue 2, July 2024, Page 329-336 PDF (387.45 K) | ||||
Document Type: Original Article | ||||
DOI: 10.21608/mnj.2024.379439 | ||||
View on SCiNiTO | ||||
Authors | ||||
Mona Elbilsha1; Ahmad Darwish2; Ahmed Masoud 3 | ||||
1Professor of Psychiatric and Mental Health Nursing, Mansoura University, Egypt | ||||
2Associate Professor of Pediatrics, Faculty of Medicine Mansoura University, Egypt | ||||
3M.D Psychiatric and Mental Health, Children Hospital of Mansoura University, Egypt | ||||
Abstract | ||||
Background: Hemoglobinopathies that require transfusions are among the most prevalent hereditary disorders in the world. Transfusion-dependent hemoglobinopathies cause unpredictable, recurrent, and frequently permanent pain, making them distinct from other pain syndromes. Objective: - This paper aims to evaluate the experience of pain in children diagnosed with transfusion dependent hemoglobinopathies. Additionally, it seeks to explore the associations between pain and various sociodemographic and clinical factors in the sample of children under study. Methodology: This cross-sectional, descriptive study comprised a sample of children between the ages of 8 and 18 years who had transfusion-dependent hemoglobinopathies. The data was obtained from the hematology clinic located at Children's Hospital, affiliated with Mansoura University in Egypt. The data was collected by the utilization of a semi-structured interview form and the implementation of the revised-Face, Leg, Activity, Cry, and Consolability scale (r-FLACC). Results: Of the children who participated in the research, two-thirds (66%) were female, and 76% had been diagnosed with beta-thalassemia. Of the children who participated in the study, over half (56%) experienced significant pain symptoms. Children with sickle cell disease who undergo twice-monthly blood transfusions and have been studied report experiencing severe pain. Conclusion: Of the children who participated in the study, over half experienced severe pain symptoms. Types of transfusion-dependent hemoglobinopathies, particularly sickle cell disease, and twice-monthly blood transfusions, have been linked with severe pain levels. Recommendations: - Regular evaluations and improved pain management programs aimed at pain reduction, would significantly enhance the well-being of pediatric patients diagnosed with transfusion-dependent hemoglobinopathies. | ||||
Keywords | ||||
Hemoglobinopathies Pain; Transfusion-dependent | ||||
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