A rare case of bilateral trigeminal palsy presenting as a complication of Sjogren syndrome | ||||
| Kasr Al Ainy Medical Journal | ||||
| Volume 23, Issue 1, January 2017 PDF (81.31 K) | ||||
| DOI: 10.4103/kamj.kamj_57_16 | ||||
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| Authors | ||||
| Ali Ilyas; Wasim T. Malik; Anam Abrar; Faleha Zafar | ||||
| Abstract | ||||
| Sjogren syndrome is a chronic disorder affecting the exocrine glands of the body, mostly lacrimal and salivary glands, resulting in sicca symptoms. Diagnosis is aided by the presence of anti-Ro and anti-La antibodies and gland biopsy showing lymphocytic infiltration. Bilateral loss of facial sensation in Sjogren syndrome (SS) has not been reported before, although unilateral trigeminal palsy as a presentation of SS has been reported in literature. A 25-year-old lady presented in the neurology clinic with complete facial numbness and vision loss for 1 month. The vision worsened, leading to complete blindness. She had dry mouth and dry eyes for the past 3 months. She was diagnosed with SS using American–European consensus Sjogren criteria. Electrophysiological blink reflex testing confirmed complete trigeminal nerve palsy. SS was treated with prednisolone, 1 mg/kg/day, with a poor response. Symptomatic treatment was given for sicca symptoms, which improved significantly. Corneal transplantation was done for visual loss, but limited improvement was seen. | ||||
| Keywords | ||||
| Blink Reflex; complete blindness; corneal transplant; Sjogren syndrome; trigeminal nerve palsy | ||||
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